This book aims to be a complete guide to diagnose, manage, and treat rare lung diseases encountered by practicing pulmonologists and trainees. It extensively covers the "more common" of the rare lung diseases, categorizing them based on developmental lung anomalies in adults, airway disorders, diffuse parenchymal lung diseases, neoplasms, rare vascular disorders, and other miscellaneous conditions. This comprehensive review facilitates the study and understanding of this complex and diverse set of disorders, focusing on differential diagnosis, evidence-based discussions of management algorithms, and thoughtful analysis of treatment options.
Key Features
* Reviews multiple rare lung diseases, including ones acquired congenitally to be expressed in old age
* Enriched with case studies and illustrations to guide respiratory physicians and trainees to devise an effective treatment plan
*Focuses on concerned investigations, with a section on the role of new procedures in management
Table of Contents:
Chapter 1: Introduction
Chapter 2: Developmental lung anomalies in adults
Rare genetic lung diseases
Chapter 3: Genetic infiltrative lung diseases
Chapter 4: Alpha-1- antitrypsin deficiency
Rare airway disorders
Chapter 5: Benign central airway disorders
Chapter 6: Bronchiolitis
Chapter 7: Allergic Bronchopulmonary Aspergillosis (ABPA)
Rare pulmonary vascular diseases
Chapter 8: Pulmonary Arteriovenous Malformations (PAVMs) and Hereditary hemorrhagic telangiectasia (HHT)
Chapter 9: Diffuse Alveolar Hemorrhage (DAH) syndromes
Chapter 10: Pulmonary Veno-occlusive Disease and Pulmonary Capillary Hemangiomatosis
Rare diffuse parenchymal lung diseases
Chapter 11: Pleuroparenchymal fibroelastosis (PPFE)
Chapter 12: Immunoglobulin G4-related lung disease
Chapter 13: Eosinophilic lung diseases
Chapter 14: Hard Metal Lung Disease and Other Rare Occupational Lung Diseases
Chapter 15: Adult Pulmonary Alveolar Proteinosis
Rare diffuse cystic lung diseases
Chapter 16: Lymphangioleiomyomatosis
Chapter 17: Lymphocytic Interstitial Pneumonia and associated Cystic Lung Diseases
Chapter 18: Birt Hogg Dube Syndrome
Chapter 19: Pulmonary Langerhans Cell Histiocytosis and other histiocytic lung diseases
Rare pulmonary neoplasms
Chapter 20: Primary pulmonary lymphoproliferative disorders
Chapter 21: Diffuse Idiopathic Pulmonary Neuroendocrine Cell Hyperplasia
Chapter 22: Pulmonary Amyloidosis
Chapter 23: Primary tracheal tumors
Rare pleural disorders
Chapter 24: Unusual causes of pleural effusions
Chapter 25: Thoracic endometriosis
Chapter 26: Tumours of the Pleura
About the Author :
Dr. Sujith V. Cherian is Associate Professor of Internal Medicine, in the Division of Critical Care, Pulmonary and Sleep Medicine at the University of Texas Health-McGovern Medical School, Houston.
Dr. Anupam Kumar is an Assistant Professor of Medicine at the Division of Pulmonary & Critical Care Medicine at Baylor College of Medicine, Houston, Texas. He is also the Director of the Interstitial Lung Diseases (ILD) Clinic at Baylor College of Medicine.
